Research Information System
Pediatrik Cerrahi Dergisi, vol.12, pp.54-56, 1998 (Scopus)
Li-Fraumeni familial cancer syndrome is a disorder that predisposes individuals to multiple forms of cancer including breast cancer, brain tumor and adrenocortical carcinoma. In this study we present a patient with Li- Fraumeni syndrome who has an extremity rhabdomyosarcoma (RMS) and phecromacytoma as a second primary. The sister of the patient showed bilateral adrenocortical tumors. In this report, the importance of the presence of a second tumor and family screening in the follow-up of childhood rhabdomyosarcoma is stressed.