Evaluation of Six Cases with ALCAPA Syndrome: a Rare but Treatable Cause of Dilated Cardiomyopathy


Ozcan N., Kizilkaya M., AKÇA T., BOSTAN Ö. M.

GUNCEL PEDIATRI-JOURNAL OF CURRENT PEDIATRICS, vol.18, no.3, pp.290-299, 2020 (ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 18 Issue: 3
  • Publication Date: 2020
  • Doi Number: 10.32941/pediatri.841394
  • Journal Name: GUNCEL PEDIATRI-JOURNAL OF CURRENT PEDIATRICS
  • Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Premier, CAB Abstracts, CINAHL, EMBASE, Veterinary Science Database
  • Page Numbers: pp.290-299
  • Bursa Uludag University Affiliated: Yes

Abstract

INTRODUCTION: Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital cardiac anomaly that can be cured with surgical treatment. It accounts for 0.25 to 0.5% of all congenital heart diseases. ALCAPA is generally asymptomatic in the neonatal period. Dilated cardiomyopathy (DCM) and mitral valve insufficiency (MVI) are detected in patients with symptoms of heart failure. ALCAPA, which is a rare cause of DCM, early surgical treatment provides quite good prognosis in the first year of life. However, mortality is high in patients who do not receive surgical treatment.