Dermatomyositis-like syndrome in a patient with X-linked agammaglobulinemia


KILIÇ GÜLTEKİN S. Ş., Ersoy F., Sanal O., Tezcan I.

Turkish Journal of Immunology, cilt.4, sa.1, ss.25-27, 1999 (SCI-Expanded) identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 4 Sayı: 1
  • Basım Tarihi: 1999
  • Dergi Adı: Turkish Journal of Immunology
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.25-27
  • Anahtar Kelimeler: Dermatomyositis-like syndrome, Hypogammaglobulinemia
  • Bursa Uludağ Üniversitesi Adresli: Evet

Özet

Patients with antibody-mediated immune deficiencies may develop a rare 'dermatomyositis-like' syndrome, which is usually progressive and fatal. We have followed-up a child with X-linked agammaglobulinemia (XLA) in whom a dermatomyositis-like syndrome was treated with high doses of intravenous immunoglobulin with short intervals. In patients with hypogammaglobulinemia dermatomyositis-like syndrome has been suggested to be a manifestation of a viral infection in a immunocompromised host.