Turkish Journal of Immunology, cilt.4, sa.1, ss.25-27, 1999 (SCI-Expanded)
Patients with antibody-mediated immune deficiencies may develop a rare 'dermatomyositis-like' syndrome, which is usually progressive and fatal. We have followed-up a child with X-linked agammaglobulinemia (XLA) in whom a dermatomyositis-like syndrome was treated with high doses of intravenous immunoglobulin with short intervals. In patients with hypogammaglobulinemia dermatomyositis-like syndrome has been suggested to be a manifestation of a viral infection in a immunocompromised host.