Dermatomyositis-like syndrome in a patient with X-linked agammaglobulinemia
Turkish Journal of Immunology, cilt.4, sa.1, ss.25-27, 1999 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 4 Sayı: 1
- Basım Tarihi: 1999
- Dergi Adı: Turkish Journal of Immunology
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.25-27
- Anahtar Kelimeler: Dermatomyositis-like syndrome, Hypogammaglobulinemia
- Bursa Uludağ Üniversitesi Adresli: Evet
Özet
Patients with antibody-mediated immune deficiencies may develop a rare 'dermatomyositis-like' syndrome, which is usually progressive and fatal. We have followed-up a child with X-linked agammaglobulinemia (XLA) in whom a dermatomyositis-like syndrome was treated with high doses of intravenous immunoglobulin with short intervals. In patients with hypogammaglobulinemia dermatomyositis-like syndrome has been suggested to be a manifestation of a viral infection in a immunocompromised host.