The retrospective evaluation of the patients diagnosed moyamoya disease at Uludag University Hospital between 2006-2010 2006-2010 Yillari arasinda Uludaǧ Üni̇versi̇tesi̇ tip fakültesi̇ hastanesi̇'nde moyamoya hastaliǧi tanisi almiş olgularin retrospekti̇f olarak deǧerlendi̇ri̇ lmesi̇


Tolgay E., Cantürk V., Bakar M., Taşkapilioǧlu Ö., Erer Özbek S., Bora I., ...More

Turk Beyin Damar Hastaliklar Dergisi, vol.17, no.3, pp.95-100, 2011 (Refereed Journals of Other Institutions) identifier

  • Publication Type: Article / Article
  • Volume: 17 Issue: 3
  • Publication Date: 2011
  • Doi Number: 10.5505/tbdhd.2011.29491
  • Title of Journal : Turk Beyin Damar Hastaliklar Dergisi
  • Page Numbers: pp.95-100
  • Keywords: Moyamoya disease

Abstract

OBJECTİVE: Moyamoya disease is usually seen in Japanese ethnicity, with an unknown ethiology and is a rare cerebral vasculopathy. We aimed to compare the patients with Moyamoya disease during the ages of childhood or adulthood in our departments with literature data. MATERIAL AND METHODS: We analysed 10 patients retrospectively according to age, gender, family history, clinical presentation, cranial MR and cerebral angiography findings and treatment who referred to the departments of Neurology and Child Neurology Clinics in Uludag University Medical Faculty between 2006-2010 years Moyamoya disease , RESULTS: 5 of 10 patients were children, 5 of them were in the adult age group. A combination of one or more symptoms of the patients with hemiparesis in 8, epileptic seizures in 6, headache in 4, and visual loss in 2, speech disorder in 3 were detected. According to cranial MR, cerebral infarction was found in 8 cases, normal findings in 1 case and intracerebral hemorrhage in 1 case. In four of the patients with cerebral infarction, middle cerebral artery occlusion was detected. All of the patients were diagnosed with the image of 'smoke' that is typical for Moyamoya disease in cerebral angiography. Nine patients were treated medically and 1 patient was treated both medically and surgically. CONCLUSION: Moyamoya disease is a rare vasculopathy. We found similar findings in our patients with the literature. As Moyamoya disease is presented with various neurological signs in different age groups, it must be kept in mind in making the differential diagnosis.