Akademik Veri Yönetim Sistemi
Turk Beyin Damar Hastaliklar Dergisi, cilt.17, sa.3, ss.95-100, 2011 (Scopus)
OBJECTİVE: Moyamoya disease is usually seen in Japanese ethnicity, with an unknown ethiology and is a rare cerebral vasculopathy. We aimed to compare the patients with Moyamoya disease during the ages of childhood or adulthood in our departments with literature data. MATERIAL AND METHODS: We analysed 10 patients retrospectively according to age, gender, family history, clinical presentation, cranial MR and cerebral angiography findings and treatment who referred to the departments of Neurology and Child Neurology Clinics in Uludag University Medical Faculty between 2006-2010 years Moyamoya disease , RESULTS: 5 of 10 patients were children, 5 of them were in the adult age group. A combination of one or more symptoms of the patients with hemiparesis in 8, epileptic seizures in 6, headache in 4, and visual loss in 2, speech disorder in 3 were detected. According to cranial MR, cerebral infarction was found in 8 cases, normal findings in 1 case and intracerebral hemorrhage in 1 case. In four of the patients with cerebral infarction, middle cerebral artery occlusion was detected. All of the patients were diagnosed with the image of 'smoke' that is typical for Moyamoya disease in cerebral angiography. Nine patients were treated medically and 1 patient was treated both medically and surgically. CONCLUSION: Moyamoya disease is a rare vasculopathy. We found similar findings in our patients with the literature. As Moyamoya disease is presented with various neurological signs in different age groups, it must be kept in mind in making the differential diagnosis.