Hairy cell leukemia presenting initially with symptoms of Behçet's disease.

Oksuz M. F., Coskun B. N., Tufan A. N., Orucoglu N., Dalkilic E., ÖZTÜRK NAZLIOĞLU H., ...More

International journal of rheumatic diseases, vol.17, no.6, pp.689-92, 2014 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 17 Issue: 6
  • Publication Date: 2014
  • Doi Number: 10.1111/1756-185x.12370
  • Journal Name: International journal of rheumatic diseases
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.689-92
  • Keywords: Behcet's disease, diagnosis, hairy cell leukemia, VASCULITIDES
  • Bursa Uludag University Affiliated: Yes


Vasculitis is relatively uncommon in lymphoproliferative disease and may predate the diagnosis of lymphoproliferative disease. Many vasculitides have been associated with hairy cell leukemia (HCL), including polyarteritis nodosa (PAN) and leukocytoclastic vasculitis. We herein report a case whose initial presentation was like Behcet's disease (BD) (arthritis, oral and genital ulcerations, papulopustular skin lesions) in addition to pancytopenia, but turned out to have HCL. Because of the overlap between their symptoms, like oral ulcerations, skin lesions, arthritis and constitutional findings, HCL and BD may mimic each other. We should keep in mind other reasons for vasculitis such as lymphoproliferative disease, especially whose who have hematological abnormalities such as pancytopenia.